ICD 10 Codes >> Diseases of the nervous system (G00-G99) G00-G99 >>Systemic atrophies primarily affecting the central nervous system (G10-G14) G10-G14 >> Hereditary ataxia G11.-

ICD 10 Code G11.4

Hereditary spastic paraplegia

2017 Billable/Specific Code

Hereditary spastic paraplegias (HSP) comprise a genetically and clinically heterogeneous group of neurodegenerative disorders characterized by varying degrees of lower limb spasticity, pyramidal weakness, hyperreflexia and hypertonic bladder involvement. Clinically, HSPs can be divided into two main groups: uncomplicated (pure) and complicated (complex) forms depending on the presence of other neurological features including ataxia, peripheral neuropathy, cognitive impairment, epilepsy, amyotrophy, retinopathy, deafness, icthyosis and extrapyramidal involvement, in addition to spastic paraparesis. Pure HSPs are characterized by slowly progressive lower extremity spasticity and weakness, often associated with hypertonic urinary disturbances, mild reduction of lower extremity vibration sense and, occasionally, of joint position sensation. Complex HSP forms are characterized by the presence of additional neurological or non-neurological features. A positive family history particularly in autosomal dominant cases is often but not always present. The diagnosis may be aided by neuroimaging and genetic testing.
  • G11.4 is a billable ICD-10 medical codes that provide a detailed representation of a patient's conditions or diagnoses.
  • ICD-10-CM codes are used for a variety of purposes, including statistics and for billing and claims reimbursement.
  • This is the American ICD 10 CM Version Of G11.4 allows for the capture of data regarding signs, symptoms, risk factors and comorbidities to better describe the clinical issue overall.

Reverse Index Lookup for ICD 10 CM CODE G11.4


The following ICD-10-CM Index entries contain back-references to ICD-10-CM G11.4:
  • Ataxia, ataxy, ataxic   R27.0
    • hereditary   G11.9
      • spastic   G11.4
    • spastic hereditary   G11.4
  • Paralysis, paralytic   G83.9
    • familial   G72.3
      • spastic   G11.4
    • spastic   G83.9
      • familial   G11.4
      • hereditary   G11.4
  • Paraplegia   G82.20
    • familial spastic   G11.4
    • hereditary, spastic   G11.4
    • spastic
      • hereditary   G11.4

  • SNOMed Terms:
    • ARSACS - autosomal recessive spastic ataxia of Charlevoix-Saguenay
    • Autosomal recessive spastic ataxia of Charlevoix-Saguenay
    • Autosomal recessive spastic ataxia of Charlevoix-Saguenay (disorder)
    • Autosomal recessive spastic paraplegia type 11
    • Autosomal recessive spastic paraplegia type 11 (disorder)
    • Autosomal recessive spastic paraplegia type 39
    • Autosomal recessive spastic paraplegia type 39 (disorder)
    • Circumscribed palmoplantar keratoderma
    • Circumscribed palmoplantar keratoderma (disorder)
    • Complicated hereditary spastic paraplegia

    • Major Diagnostic Categories
      M.D.C

      • MDC Category : 01
      • MDC Type : Medical
      • Description : Diseases and Disorders of the Nervous System

    • Medicare Severity-Diagnosis Related Groups
      MS-DRG

      • DRG Range: 058-060
        • 058 -- MULTIPLE SCLEROSIS & CEREBELLAR ATAXIA W MCC

        • Notice: Trying to get property of non-object in /home/bindmedic/public_html/libs/php/main_class.php on line 395
          59 --
        • 060 -- MULTIPLE SCLEROSIS & CEREBELLAR ATAXIA W/O CC/MCC

    • Clinical Classifications Software
      CCS

      • CCS Category Number : 81
      • Description : Other hereditary and degenerative nervous system conditions
      • Multi CCS Level 1 Number : 6
      • Level 1 Description : Diseases of the nervous system and sense organs
      • Multi CCS Level 2 Number : 6.2
      • Level 2 Description : Hereditary and degenerative nervous system conditions

    • Prevention Quality Indicators (admissions for 'ambulatory care sensitive conditions')
      ACSC

      G11.4 ICD CODE is not Assigned For ACSA Admit

    • New York University Emergency Department visit severity algorithm
      NYU ED

      Non-emergent - 0%
      Emergent/Primary Care Treatable - 0%
      Emergent - ED Care Needed - Preventable/Avoidable - 0%
      Emergent - ED Care Needed - Not Preventable/Avoidable - 0%
      Primary diagnosis of injury 0%
      Primary diagnosis of mental health problems 0%
      Primary diagnosis of substance abuse 0%
      Primary diagnosis of Alcohol 0%
      Unclassified 100%

    Neuromuscular disorders affect the nerves that control your voluntary muscles. Voluntary muscles are the ones you can control, like in your arms and legs. Your nerve cells, also called neurons, send the messages that control these muscles. When the neurons become unhealthy or die, communication between your nervous system and ...

    Also called: Hemiplegia, Palsy, Paraplegia, QuadriplegiaParalysis is the loss of muscle function in part of your body. It happens when something goes wrong with the way messages pass between your brain and muscles. Paralysis can be complete or partial. It can occur on one or both sides of your body. ...

    Silver syndrome belongs to a group of genetic disorders known as hereditary spastic paraplegias. These disorders are characterized by progressive muscle stiffness (spasticity) and, frequently, development of paralysis of the lower limbs (paraplegia). Hereditary spastic paraplegias are divided into two types: pure and complex. Both types involve the lower limbs; ...

    Spastic paraplegia type 31 is one of a group of genetic disorders known as hereditary spastic paraplegias. These disorders are characterized by progressive muscle stiffness (spasticity) and the development of paralysis of the lower limbs (paraplegia) caused by degeneration of nerve cells (neurons) that trigger muscle movement. Hereditary spastic paraplegias are ...

    Spastic paraplegia type 3A is one of a group of genetic disorders known as hereditary spastic paraplegias. These disorders are characterized by muscle stiffness (spasticity) and weakness in the lower limbs (paraplegia). Hereditary spastic paraplegias are often divided into two types: pure and complex. The pure types involve only the ...

    Spastic paraplegia type 15 is part of a group of genetic disorders known as hereditary spastic paraplegias. These disorders are characterized by progressive muscle stiffness (spasticity) and the development of paralysis of the lower limbs (paraplegia). Spastic paraplegia type 15 is classified as a complex hereditary spastic paraplegia because it involves all ...

    Spastic paraplegia type 11 is part of a group of genetic disorders known as hereditary spastic paraplegias. These disorders are characterized by progressive muscle stiffness (spasticity) and the development of paralysis of the lower limbs (paraplegia). Hereditary spastic paraplegias are divided into two types: pure and complex. The pure types involve ...

    Spastic paraplegia type 7 is part of a group of genetic disorders known as hereditary spastic paraplegias. These disorders are characterized by progressive muscle stiffness (spasticity) and the development of paralysis of the lower limbs (paraplegia). Hereditary spastic paraplegias are divided into two types: pure and complex. The pure types involve ...

    Spastic paraplegia type 4 is part of a group of genetic disorders known as hereditary spastic paraplegias. These disorders are characterized by progressive muscle stiffness (spasticity) and the development of paralysis of the lower limbs (paraplegia). Hereditary spastic paraplegias are divided into two types: pure and complex. The pure types involve ...

    Spastic paraplegia type 2 is part of a group of genetic disorders known as hereditary spastic paraplegias. These disorders are characterized by progressive muscle stiffness (spasticity) and the development of paralysis of the lower limbs (paraplegia). Hereditary spastic paraplegias are divided into two types: pure and complex. The pure types involve ...

    Mutant spastin proteins promote deficits in axonal transport through an isoform-specific mechanism involving casein kinase 2 activation.

    Leo L, Weissmann C, Burns M, Kang M, Song Y, Qiang L, Brady ST, Baas PW, Morfini G

    Clinical features and genotype-phenotype correlation analysis in patients with ATL1 mutations: A literature reanalysis.

    Zhao GH, Liu XM

    Defects in ER-endosome contacts impact lysosome function in hereditary spastic paraplegia.

    Allison R, Edgar JR, Pearson G, Rizo T, Newton T, Günther S, Berner F, Hague J, Connell JW, Winkler J, Lippincott-Schwartz J, Beetz C, Winner B, Reid E

    A novel mutation in KIF5A in a Malian family with spastic paraplegia and sensory loss.

    Guinto CO, Diarra S, Diallo S, Cissé L, Coulibaly T, Diallo SH, Taméga A, Chen KL, Schindler AB, Bagayoko K, Simaga A, Blackstone C, Fischbeck KH, Landouré G

    Targeted high throughput sequencing in hereditary ataxia and spastic paraplegia.

    Iqbal Z, Rydning SL, Wedding IM, Koht J, Pihlstrøm L, Rengmark AH, Henriksen SP, Tallaksen CM, Toft M

    Hereditary spastic paraplegia caused by compound heterozygous mutations outside the motor domain of the KIF1A gene.

    Krenn M, Zulehner G, Hotzy C, Rath J, Stogmann E, Wagner M, Haack TB, Strom TM, Zimprich A, Zimprich F

    NT5C2 novel splicing variant expands the phenotypic spectrum of Spastic Paraplegia (SPG45): case report of a new member of thin corpus callosum SPG-Subgroup.

    Elsaid MF, Ibrahim K, Chalhoub N, Elsotouhy A, El Mudehki N, Abdel Aleem A

    SPG2 mimicking multiple sclerosis in a family identified using next generation sequencing.

    Rubegni A, Battisti C, Tessa A, Cerase A, Doccini S, Malandrini A, Santorelli FM, Federico A

    Pla2g6 mutations associated with a continuous clinical spectrum from neuroaxonal dystrophy to hereditary spastic paraplegia.

    Ozes B, Karagoz N, Schüle R, Rebelo A, Sobrido MJ, Harmuth F, Synofzik M, Pascual SI, Colak M, Ciftci-Kavaklioglu B, Kara B, Ordóñez-Ugalde A, Quintáns B, Gonzalez MA, Soysal A, Zuchner S, Battaloglu E

    Evaluating the Calling Performance of a Rare Disease NGS Panel for Single Nucleotide and Copy Number Variants.

    Cacheiro P, Ordóñez-Ugalde A, Quintáns B, Piñeiro-Hermida S, Amigo J, García-Murias M, Pascual-Pascual SI, Grandas F, Arpa J, Carracedo A, Sobrido MJ

    Child Group Time: 0.970663070679